Intraocular Lens Subluxation in Marfan Syndrome
Bolaños-Jiménez Rodrigo*, 1, 2, López-Lizárraga E Paulina 3, March de R Francesc 4, 5, Telich-Tarriba J Eduardo 6, Navas Alejandro 7
Identifiers and Pagination:Year: 2014
First Page: 48
Last Page: 50
Publisher ID: TOOPHTJ-8-48
Article History:Received Date: 18/7/2014
Revision Received Date: 21/7/2014
Acceptance Date: 21/7/2014
Electronic publication date: 19 /9/2014
Collection year: 2014
open-access license: This is an open access article licensed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted, non-commercial use, distribution and reproduction in any medium, provided the work is properly cited.
Ectopia lentis (EL) is a major criteria for the diagnosis of Marfan syndrome, it may vary from an asymptomatic mild displacement to a significant subluxation that places the equator of the lens in the pupillary axis. The purpose of this work is to present the case of a patient with Marfan syndrome who received treatment for subluxation at our institution.
Case Report :
A 51-year-old female diagnosed with Marfan syndrome presented to the emergency department with bilateral eye redness, foreign body sensation and crusting around the eyes on awakening. She had the following history of cardiac and ophthalmologic complications, including: 1. Lens subluxation 2. High myopia 3. Aortic root dilation, 4. Mitral valve prolapse and 5. Tricuspid insufficiency.
The ophthalmological management of Marfan patients is challenging and periodical follow-up is needed. Surgical versus conservative management is controversial, each case needs to be evaluated individually to analyze the risks and benefits of the procedures.