Intraocular Lens Subluxation in Marfan Syndrome



Bolaños-Jiménez Rodrigo*, 1, 2, López-Lizárraga E Paulina 3, March de R Francesc 4, 5, Telich-Tarriba J Eduardo 6, Navas Alejandro 7
1 Department of Opthalmology, Regional Hospital Adolfo López Mateos, ISSSTE, Mexico City, Mexico
2 Research Unit, Institute of Ophthalmology, Fundación Conde de Valenciana, Mexico City, Mexico
3 Department of Anterior Segment, Institute of Ophthalmology, Fundación Conde de Valenciana, Mexico City, Mexico
4 Department of Vitreoretinal Surgery, Institute of Ophthalmology, Fundación Conde de Valenciana, Mexico City, Mexico
5 Department of Anterior Segment, Dr. Luis Sánchez Bulnes Hospital, Asociación Para Evitar la Ceguera en México, Mexico City, Mexico
6 National Institute of Cardiology "Ignacio Chávez", Mexico City, Mexico
7 Department of Cornea and Refractive Surgery Institute of Ophthalmology, Fundación Conde de Valenciana, Mexico City, Mexico


Article Metrics

CrossRef Citations:
0
Total Statistics:

Full-Text HTML Views: 514
Abstract HTML Views: 350
PDF Downloads: 162
Total Views/Downloads: 1026
Unique Statistics:

Full-Text HTML Views: 342
Abstract HTML Views: 218
PDF Downloads: 107
Total Views/Downloads: 667



© Rodrigo et al.; Licensee Bentham Open.

open-access license: This is an open access article licensed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted, non-commercial use, distribution and reproduction in any medium, provided the work is properly cited.

* Address correspondence to this author at the Department of Opthalmology, Regional Hospital Adolfo López Mateos, ISSSTE, Mexico City, Mexico; Fax: 525552345685; E-mail: rodrigoboji88@gmail.com


Abstract

Purpose :

Ectopia lentis (EL) is a major criteria for the diagnosis of Marfan syndrome, it may vary from an asymptomatic mild displacement to a significant subluxation that places the equator of the lens in the pupillary axis. The purpose of this work is to present the case of a patient with Marfan syndrome who received treatment for subluxation at our institution.

Case Report :

A 51-year-old female diagnosed with Marfan syndrome presented to the emergency department with bilateral eye redness, foreign body sensation and crusting around the eyes on awakening. She had the following history of cardiac and ophthalmologic complications, including: 1. Lens subluxation 2. High myopia 3. Aortic root dilation, 4. Mitral valve prolapse and 5. Tricuspid insufficiency.

Conclusion :

The ophthalmological management of Marfan patients is challenging and periodical follow-up is needed. Surgical versus conservative management is controversial, each case needs to be evaluated individually to analyze the risks and benefits of the procedures.

Keywords: Capsular tension ring, intraocular lens subluxation, zonular dyalisis, zonular instability.